文档介绍:ConceptionofILD(DPLD)ILDisaspectrumofnon-infectious,non-(DiffuseParenchymalLungDisease):bronchiolesandparenchymaMedicalTerminologyInterstitiallungdisease(ILD)间质性肺病Diffuseparenchymallungdisease(DPLD)弥漫性肺实质肺病Idiopathicinterstitialpneumonia(IIP)特发性间质性肺炎Idiopathicpulmonaryfibrosis(IPF)特发性肺纤维化Usualinterstitialpneumonia(UIP)普通性间质性肺炎Non-specificinterstitialpneumonia(NSIP)anizingpneumonia(COP)隐原性机化性肺炎Acuteinterstitialpneumonia(AIP)急性间质性肺炎Desquamativeinterstitialpneumonia(DIP)脱屑性间质性肺炎Respiratorybronchiolitis-associatedinterstitiallungdisease(RB-ILD)呼吸细支气管炎间质性肺炎Lymphocyticinterstitialpneumonia(LIP)淋巴细胞性间质性肺炎Granulomatous肉芽肿的Sarcoidosis结节病Lymphangioleiomyomatosis淋巴管平滑肌瘤Histiocytosis(HX)组织细胞增多症Reticular网格状Nodule(nodular)结节Groundglassopacity(GGO)磨(毛)bing蜂窝Diffusioncapacity弥散量Bronchoalveolarlavarge(BAL)肺泡灌洗Transbronchoscopiclungbiopsy(TBLB)经气管镜肺活检Crackle爆裂音ClassificationofILDbyATS/ERS2002IDIOPATHICINTERSTITIALPNEUMONIA(IIP)GRANULOMATOSISsarcoidosisHypersensitivepneumonitisWegener'sgranulomatosis,-upationallungdisease(pneumoconiosis)Drug-ountsfor100,000hospitaladmissionsyearly15%(5/100,000)intheUSNewMexico:,,,,%--HistoryLengthOfIllnessAndClinicalCourseAcuteonset:daystoweeksAcuteinterstitialpneumoniaAcutepneumonitisfromcollagenvasculardisease(especiallySLE)anizingpneumoniaDrugsDiffusealveolarhemorrhage(弥漫性肺抛出血)Eosinophiliclungdisease(嗜酸性粒细胞肺病)Hypersensitivitypneumonitis(过敏性肺炎)Subacute:weekstomonthsCollagenvasculardisease–anizingpneumoniaDrugsSubacutehypersensitivitypneumonitisChronic:monthstoyearsIdiopathicpulmonaryfibrosisChronichypersensitivitypneumonitisCollagenvasculardi