文档介绍：询庭水管扩大综合征8例临床分析
【关键词】，前庭水管
【摘要】目的探讨单纯前庭水管扩大综合征（LVAS）的发病机制、临床表现、诊断治疗 及预防。方法冋顾性分析我院LVAS 8例（14耳）患者的临床特点、听力学及CT检查， 并复****文献。结果8例经CT检查结合临床表现均确诊为LVAS。结论LVAS为前庭水管先 天发育宽大畸形，出生后或少儿时出现感音神经性耳聋，高分辨螺旋CT可以确诊。目前保 守治疗缺乏特效性，可以选择性行电子耳蜗植入术。
【关键词】前庭水管；扩大；畸形；井喷
Enlarged vestibular aqueduct syndrome:a clinical analysis of 8 cases
ZHANG En-dong,LIU Xin-yi,SUN Cai-bo,et al.
The Second Hospital of Weihai,Weihai 264200,China
【Abstract] Objective To evaluate the pathogenesis,clinical feature,diagnosis,prevention and treatment of the enlarged vestibular aqueduct The clinical characters,audiology and CT test of 8 patients with the enlarged vestibular aqueduct syndrome were studied addition the literatures were 8 cases were all diagnosed as the enlarged vestibular aqueduct EVAS is the congenital enlarged abnormalities of vestibular aqueduct,with the sensorineural hearing loss after birth or in childhood,that are diagnosed by the high-resolution compution conservative treatment isn't the most effective method,but cocholear implantation can be elected.
[Key words] vestibular aqueduct； enlarged;abnormalities； pulsatile clear fluid gusher
前庭水管扩大综合征（large vestibular aqueduct syndrome,LVAS）是指前庭水管（VA）先天发育宽 夫 不伴其他内耳畸形，以波动性感音神经性耳聋及前庭功能障碍为主耍临床表现的先天性 疾病[1]。Valvassori [2] 1978年首次报道此病,逐渐引起耳科学者的重视,国内20世纪 90年代渐有报道。我院1996年1月〜2002年