文档介绍：支气管扩张(bronchiectasis ) 呼吸科吕寒静何谓支气管扩张? ?支气管由于管壁的肌肉、软骨和弹性组织结构破坏引起官腔的扩张和变形。 Bronchiectasis Definition ? Bronchiectasis is a chronic inflammatory or degenerative condition of one or more bronchioles of the lungs marked by dilatation. 为什么会支气管扩张? ?支气管感染:细菌、结核、曲霉菌感染阻塞支扩为什么会支气管扩张? ?支气管被牵拉: 结核后?支气管阻塞:感染、异物、肿瘤(内长、外压) 为什么会支气管扩张? ?支气管先天发育障碍和遗传因素: 1. 巨大气管-支气管症( tracheobronchomegaly) 2. Kartagener 综合征(不动纤毛综合征,immotile cilia syndrome) 3. 副鼻窦-支气管综合征( sinobronchial syndrome ) The sinobronchial syndrome consists of chronic sinusitis and chronic nonspecific inflammation of the lower airways, typically chronic bronchitis, bronchiectasis and diffuse panbronchiolitis. This airway disease of unknown etiology is not related to smoking. It mon in Japan and is poorly described in western countries. We report a case in a non-Asian patient. The known efficacy of long-term low-dose erythromycin therapy justifies careful diagnosis of sinobronchial syndrome in patients of non-Asian ethnic origin. 4. 先天性软骨缺失症( congenital cartilage deficiency ) 5. 支气管肺隔离症(bronchopulmanary sequestration) 支气管扩张有哪些病理特点? ?支气管壁的肌肉、软骨和弹性组织结构破坏引起管腔扩大。(柱状、囊状) ?鳞状上皮取代纤毛柱状上皮。?杯状细胞、粘液细胞增生。?毛细血管扩张。支气管扩张有哪些病生特点? 与病变范围有关?阻塞性通气功能障碍?阻塞为主的混合性通气功能障碍? V/Q 比例失调?肺源性心脏病、右心衰竭支气管扩张有哪些临床特点? ?长期咳嗽、咳痰:痰液可分层?反复咯血?反复造成相应部位的肺炎?慢性感染中毒症状:类似慢性肺脓肿?固定部位持久的湿啰音?肺气肿、肺心病的表现?杵状指(趾) Bronchiectasis symptoms ? The most typical symptom is a chronic cough that produces thick, white or green sputum and may be the first symptom of bronchiectasis. Symptoms begin usually after a respiratory infection.